Isifo sikaVon Willebrand enjeni

Ugqirha wezilwanyana ovavanya inja.

La Isifo seVon Willebrand sisifo esizuze ilifa esichaphazela ngamandla ukuhamba kwegazi, njengoko sibonakaliswa kukusilela kweVon Willebrand factor, iglycoprotein evumela iiplatelets ukuba zinamathele kwimithambo yegazi ngexesha lenkqubo yokujiya. Oku kubangela ukopha rhoqo kunye nokuphola okunzima kwenxeba.

Le yinto engathandekiyo enxulumene ukujiya kwegazi Ixhaphake kakhulu ezinjeni, enguMalusi waseJamani, iGolden Retriever, iPoodle, iDoberman kunye neShetland Sheepdog ezinye zezona ntlobo zixhaphakileyo kuzo. Ilifa ngokwendalo, kubangelwa kukutshintsha kwemfuza okunokwenzeka kwindoda okanye kwabasetyhini ngokungacacanga, kwaye kuzibonakalisa ngeempawu ezinje ngezi zilandelayo:

• Ukopha kwiintsini nakwimpumlo.
• Ukopha kwilindle nasemchameni.
• Ukurhawuzelela ulusu ngaphandle kwesizathu.
• Ukopha kakhulu kwilonda elincinci.
• Ukopha ngokugqithileyo kwilungu lobufazi ngexesha lobushushu okanye lokuhambisa.
• Ukuphelelwa kwegazi.

Le miqondiso yenzeka ukusukela kunyaka omnye ubudala kwaye ngokuxhomekeke kubunzulu bayo inokuba yinxalenye yeVon Willebrand Type Type 1, Type 2 okanye Type 3. Ngethamsanqa, kwiimeko ezininzi iimpawu inobulali kakhulu, kangangokuba amaxesha amaninzi esi sifo asifumaneki de isilwanyana singafakwanga kuqhaqho. Nangona kunjalo, ukuba sikrokrela ukuba inja yethu inokuba nayo, into elungileyo ekufuneka yenziwe kukuya kugqirha wezilwanyana.

Esi sifo sifumaneka kuvavanyo olwaziwa njenge "Ukuphuma kwegazi kwi-mucosa yomlomo" (TSMB), kwaye iqulathe ukujonga ukuba kuthabatha ixesha elingakanani inxeba elincinci kwiintsini zenja ukuba lijiye. Kufuneka ihlale isenziwa ngugqirha wezilwanyana, oya kuthi enze uvavanyo lwegazi ukufumanisa ipesenti yeVon Willebrand factor ekhoyo kuyo. Uyakwenza uvavanyo lwe-DNA ukuchonga izinja ezinezi mpawu kunye nabathwali besifo; Olu vavanyo lolona luthembekileyo kuzo zonke isifo.

Akukho lunyango loku kungaqhelekanga, kodwa iimpawu zakho zinokulawulwa ngempumelelo enkulu ngokusebenzisa amayeza. Uninzi lwexesha, inikwa ngaphambi okanye emva kotyando, nasemva kokulimala okanye ingozi. Kwiimeko ezinzima kakhulu, utofelo-gazi luyimfuneko.


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