Ukuba unayo imbethi manqindi kwaye uziva ngathi iyadina ngokukhawuleza, uzama ukudlala nayo kwaye ngequbuliso iphelelwe ngamandla, isifo entliziyweni kwaye kukuba kolu luhlobo enye yezona ngxaki zixhaphakileyo yile arrhythmogenic cardiomyopathy yomdlalo wamanqindi.
La arrhythmogenic boxer cardiomyopathy Sisifo esosulelayo esidluliselwa ngendlela ye-autosomal ephezulu, oku kuchaphazela i-ventricle elungileyo, ihlala ibonakalisa ukuba mdala, esi sisifo esenziwa ngumxube wezinto ezininzi ezinje ngembali yosapho, ubukho be I-syncope kunye ne-ventricular arrhythmias.
Ukuphelelwa ngamandla kwiBoxer
Yiyo Inkqubo yokwehla kwe-myocardium eyandulela ukubonakala kwe-arrhythmias, ukufa ngesiquphe, phakathi kwabanye kwaye kukuba ukungena kunye ne-atrophy ye-myocyte iyenziwa, ngaphandle kwento eyenziweyo.
Esi sisifo ihlala ibonakala phakathi kweminyaka emithandathu nesibhozo kwaye kwimeko ezininzi, izinja ezinesifo esi ngenxa yesifo kwaye zihlala zivela kwimfuza emihlanu echaphazela ii-desmosomes.
Kwezi meko zikhona iintlobo ezintathu zezigulana, izinja ze-asymptomatic ezine-ventricular arrhythmias, izinja ezine-tachyarrhythmias, kunye nezinja ezine-systolic dysfunction.
Ukuchongwa kwesifo
Ukuchongwa kwesi sifo kwenziwa ngokufunda izinto ezininzi ezinje nge imvelaphi yosapho, ukufumanisa i-ventricular extrasystoles, ukunganyamezelani kunye ne-tachycardia ye-ventricular.
Olona phando lubaluleke kakhulu olwenziwe sisifundo se-pathological ye-myocardium.
Uvavanyo lomzimba luhlala luqhelekile, kodwa ngamanye amaxesha uphawu lokuqala lweklinikhi lulo ukufa ngesiquphe kwesilwanyana, i-arrhythmias inokuviwa, kunye nokumbombozela kokubuyiswa kwemitral, i-tachypnea, i-edema, ukubetha okuhle kwe-jugular, kunye ne-ascites kubonwa rhoqo kwizinja ezinokungaphumeleli kwe-systolic.
IX-reyi kunye nesifundo se-echocardiographic zihlala ziqhelekile kuba zihlala ziyingxaki yombane wentliziyo, IX-reyi ayisoloko ibonisa iingxaki Ngaphandle kokuba kukho ukusilela kwe-systolic, akukho lutshintsho kulwakhiwo luhlala lubonwa kwi-echocardiography.
Arrhythmia ezinjeni
I-electrocardiogram ibonisa izakhiwo ze-ventricular zasekunene, Umda oshiyekileyo kukuba ii-arrhythmias zivela qho imini yonke, yiyo loo nto iHolter isetyenzisiwe kwaye kukho ngoku iimvavanyo zofuzo ezinokwazi ukuchonga utshintsho kwimfuza olunxulunyaniswa nesi sifo.
Ngokuqinisekileyo unemibuzo ngaye Ingxelo kaHolter, kodwa eyona nto ibalulekileyo ekufuneka siyazi kukuba ii-arrhythmias zezi zinja zihlala ziphakathi ukuze ugqirha wezilwanyana angayiva, kodwa irekhodi likaHolter livumela uvavanyo ukuba lwenziwe kwixesha elide ngaphakathi kwimeko entle yesigulana, oku ivumela isifundo Ngaphandle kokuhamba noxinzelelo ezi zilwanyana luziva xa lisiya kudibana.
Oku kufana nokwenza i-electrocardiogram kodwa ixesha elide kwaye kwindawo eqhelekileyo yenja, ke iya kuziva ikhuselekile, kwaye akukho mfuneko yokuchitha iphepha elininzi kolu phononongo. Umsebenzi ugcinwa kwimemori eya kuthi kamva ikhutshelwe kwikhompyuter, ekucetyisweni yenza idayari yenja, ukulungiselela ukuqhuba kofundo kunye nokuqinisekisa ukuba ugqirha wezilwanyana uyayazi indlela eqhube ngayo isilwanyana sakho kwaye angakunceda ukuba usinike unyango olungcono.
Iingcali zentliziyo zicebisa ukuba kwenziwe olu vavanyo minyaka le kwiimbethi manqindi kunye nokuqala kwiminyaka emithathu ubudala.
Kodwa kufanele kuqatshelwe ukuba a Isifundo sikaHolter Ngokwesiqhelo kwinja endala kuneminyaka emi-4 ayishiyi bucala ukubonakala kwesi sifo kwaye uninzi lwezi zinja zichaphazeleka yile meko azihlali zikhulisa ukungasebenzi kakuhle kwe-systolic okanye uhlobo oluthile lokusilela kwentliziyo, ke unyango luhlala lusetyenziswa antiarrhythmics yangaphakathi.
Phakathi kwezona zikhokelo zixhaphakileyo zonyango ukuze sikwazi ukunciphisa i-PVCs sifumana I-Sotalol kunye ne-mexiletine. Kodwa kufanelekile ukuba sikhankanye ukuba injongo yonyango isekwe kulawulo lokuphindaphinda kwe-arrhythmias embi ukunqanda ukufa ngesiquphe.